Three cases with papillon-lefevre syndrome
Derya Uçmak 1 * , Yavuz Yeşilova, Mehmet Nurullah Er, Tuba Dal
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1 Bismil Devlet Hastanesi, Dermatoloji Kliniği, Diyarbakır-Turkey
* Corresponding Author

Abstract

Papillon-Lefevre Syndrome is an extremely rare genetic disorder that typically effects infants of approximately one to 5 years of age. Papillon-Lefevre Syndrome is characterized by the development of palmar-plantar hyperkeratosis and early loss of the primary (deciduous) and permanent teeth due to rapidly progressive periodontopathy. The primary (deciduous) teeth frequently become loose and fall out by about five years of age. In the general population, the disorder occurs in approximately one to 4 individuals per 1.000.000. Here we present a Papillon- Lefevre Syndrome case, which is rarely seen, with a review of the literature.

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This is an open access article distributed under the Creative Commons Attribution License (CC BY 4.0) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Article Type: Case Report

https://doi.org/10.5799/ahinjs.01.2011.02.0244

J Clin Exp Invest, 2011 - Volume 2 Issue 2, pp. 222-224

Publication date: 14 Jun 2011

Article Views: 1907

Article Downloads: 1545

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