Anesthetic management in a pediatric patient with Noonan syndrome, hypopituitarism and hypothyroidism: A case report
Abdulkadir Yektaş 1 * , Ramazan Ahmet Altunbay, Ayşin Alagöl
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1 Bağcılar Eğitim ve Araştırma Hastanesi İstanbul, Turkey* Corresponding Author

Abstract

Noonan syndrome is a genetically transmitted autosomal dominant disorder characterized by various anatomic anomalies and pathophysiologic derangements. Associ­ated anomalies include hyperthelorism, ptosis, microgna­thia, downward sloping palpebral fissures, low-set ears, abnormal helix of ear, deeply grooved philtrum, short and/ or webbed neck, low hairline and cervical vertebral anom­alies. Patients with Noonan syndrome are known to pres­ent with challenging airways. Tracheal intubation can be difficult because of airway and cervical vertebral anoma­lies and bag mask ventilation may be difficult because of asymmetrical face. We present a case of anesthetic man­agement for Noonan syndrome.

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This is an open access article distributed under the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Article Type: Case Report

J Clin Exp Invest, 2013, Volume 4, Issue 2, 238-241

https://doi.org/10.5799/ahinjs.01.2013.02.02275

Publication date: 13 Jun 2013

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